维普期刊资源整合服务平台（V6.5）

20篇 您的检索式：作者名="Ijlst"

选中清除导出查看参考文献查看引证文献引用追踪共1页首页上一页第1页下一页末页 /1 跳转

	题名	作者	年代	出处	被引量
1	Metabolite transport across the Peroxisomal membrane 显示文摘	Visser W F van Roermund C W T Ijlst L	2007	Biochem J2007，401，2：	1
2	Inhibition of hepatic carnitinepalmitoyl-transferase I ( CPT IA) by valproyl-CoA as a possiblemechanism of valproate-induced steatosis显示文摘	Aires CC Ijlst L Stet F	2010	Biochem Pharmacol2010，79，5：	1
3	The human peroxisomal ABC half transporterALDP functions as a homodimer and accepts acyl- CoA esters 显示文摘	van Roermund CW Visser WF Ijlst L	2008	FASEB J2008，22，12：	1
4	Molecular basis of long - chain 3 - hydroxyacyl - CoA dehydrogenase deficiency : identification of the major disease - causing mutation in the alpha - subunit of the mitechondrial trifunctional protein 显示文摘	IJlst L Wanders RJA Ushikubo S	1994	Biechirn Biophys Acta1994，12，15：	1
5	Sudden infant death and long-chain 3-hydroxyacyl-CoA dehydrogenase显示文摘	Wanders RJA Duran M Ijlst L	1989	Lancet1989，2，：	1
6	Brown-Vialetto-Van Laere and Fazio Londe syndrome is associated with a riboflavin transporter defect mimicking mild MADD: a new inborn error of metabolism with potential treatment 显示文摘	Bosch AM Abeling NG Ijlst L	2011	J Inherit Metab Dis2011，34，1：	1
7	Clinical, biochemical and moleculargenetic characteristics of 19 patients with the Sjgren -Larsson syndrome 显示文摘	Willemsen MA IJlst L Steijlen PM	2001	Brain2001，124，7：	1
8	Molecularbasisoflongchain3-hydroxyacyl-CoA dehydrogenase deficiency:identification of the major disease-causing mutation in the alpha-subunit of the mito-chondrial trifunctional protein显示文摘	Ijlst L Wanders RJ Ushikubo S	1994	Biochim Biophys Acta1994，1215，：	1
9	New insights on themechanisms of valproate-induced hyperammonemia: inhibitionof hepatic N-acetylglutamate synthase activity by valproyl-CoA显示文摘	Aires CC van Cruchten A Ijlst L	2011	J Hepatol2011，55，2：	1
10	New insights on the mechanisms of valproate-induced hyperammonemia , inhibition of hepatic nacetylglutamate synthase activity by valproylCoA显示文摘	Aires CC van Cruchten A Ijlst L	2011	J Hepatol2011，55，2：	1
11	The human peroxisomal ABC half transporter ALDP functions as a homodimer and accepts acyl-CoA esters显示文摘	van Roermund C W Visser W F Ijlst L van Cruchten A Boek M Kulik W	2008	FASEB J2008，22，：	1
12	Metabolite transport across the peroxisomal membrane 显示文摘	Visser W F van Roermund C W Ijlst L	2007	Biochem J2007，401，2：	1
13	New insights on the mechanisms of valproate-induced hyperammonernia , inhibition of hepatic N -acetylglutamate synthase activity by valproyl-CoA 显示文摘	Aires CC van Cruehten A Ijlst L	2011	J Hepatol2011，55，2：	1
14	Carnitine palmitoyl transferase 2 and camitine/acylcarnitine translocase are involved in the mitochondrial synthesis and export of acylcarnitines显示文摘	Violante S Ijlst L Te Brinke H		0，，05：	1
15	Inhibition of hepatic carnitine palmitoyl-transferase I (CPT IA) by valproyl-CoA as a possi- ble mechanism of valproate-induced steatosis 显示文摘	Aires CC Ijlst L Stet F	2010	Biochem Pbarmacol2010，79，5：	1
16	Subcellular localization and physiological role of alpha-methylacyl-CoA racemase显示文摘	Ferdinandusse S Denis S IJlst L	2000	J Lipid Re''s2000，41，11：	1
17	Sudden infant death and long-chain 3-hydroxyacyl-CoA dehydrogenase显示文摘	Wanders RJA Duran M IJlst L	1989	Lancet1989，2，：	1
18	Clinical variability of isovaleric acidemia in a genetically homogeneous population显示文摘	Dercksen M Duran M Ijlst L		0，，06：	1
19	Primary plasmalemmal carnitine transporter defect manifested with dicarboxylic aciduria and impaired fatty acid oxidation显示文摘	N. L. S. Tang J. Hui L. K. Law K. F. To J. P. N. Ruiter L. IJlst R. J. A. Wanders C. S. Ho T. F. Fok P. M. P. Yuen N. M. Hjelm	1998	Journal of Inherited Metabolic Disease1998，，4：	1
20	Common missense mutation G1528C mution in long chain 3-hydroxyacyl-CoA dehydrogenase deficiency 显示文摘	IJlst L Ruiter JPN Hoovers JMN	1996	J Clin Invest1996，98，：	1

返回顶部每页显示：

共1页首页上一页第1页下一页末页 /1 跳转

互联网出版许可证新出网证(渝)字10号全国400电话 - 免长途话费

用户提示