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| 1 | Juvenile hemochromatosis:HAMP mutation and severe iron overload treated with phlebotomies and deferasirox显示文摘Juvenile hemochromatosis(JH) is a rare condition classified as an autosomal recessive disorder that leads to severe iron absorption. JH usually affects people under the age of 30 and presents symptoms such as chronic liver damage,hypogonadotropic hypogonadism,cardiac diseases and endocrine dysfunctions. The present case reports a 29-year-old Brazilian woman with JH condition due to HAMP mutation(g.47G>A),treated with phlebotomies and deferasirox. She presented symptoms such as weakness,skin hyperpigmentation,joint pain in the shoulders and hands and amenorrhea. First laboratory tests showed altered biochemical parameters [serum ferritin(SF): 5696 ng/mL,transferrin saturation(TS): 85%]. After sessions of phlebotomies(450 mL every 15 d),the patient presented partial symptomatic improvements and biochemical parameters(SF: 1000 ng/mL,Hb: 11 g/dL). One year later,deferasirox(15 mg/kg per day) was introduced to the treatment,and the patient showed total symptomatic improvement,with significant clearing of the skin,SF: 169 ng/mL,and TS: 50%. Furthermore,after the combined deferasirox-phlebotomy therapy,magnetic resonance imaging measurements revealed normalized level for liver iron(30 μmol/g; reference value < 36 μmol/g). In conclusion,combined deferasirox-phlebotomy treatment was able to normalize iron levels and improve symptoms. | Manuel A Lescano Letícia C Tavares Paulo C J L Santos | 2017 | World Journal of Clinical Cases2017，5，10： | 2 |
| 2 | Comparative study of propylene polymerization using Me2Si(Rind)2ZrCl2/SiO2-SMAO/AlR3 and Me2Si(RInd)2ZrCl2/MAO(R=Me, H)显示文摘 | Franceschini F C da R Tavares T T dos Santos J H Z | 2007 | Polymer2007，48，7： | 1 |
| 3 | Optimization of Fenton's oxidation of chemical laboratory wastewaters using the response surface methodology 显示文摘 | Benatti C T Tavares C R G Guedes T A | 2006 | Journal of Environmental Management2006，80，： | 1 |
| 4 | Tuberculosis deaths in a tertiary hospital in Goiania, Brazil: a descriptive study 显示文摘 | Tavares C Bacelar Acioli Lins T Junqueira Kipnis AP | 2013 | Infez Med2013，21，4： | 1 |
| 5 | Immobilization of commercial laccase on spent grain显示文摘 | da Silva A M Tavare A P M Rocha C M R | 2012 | Process Biochem2012，479，7： | 1 |
| 6 | Effect of experimental conditions on cogasification of coal,biomass and plastics wastes with air/steam mixtures in a fluidized-bed system显示文摘 | PINTO F FRANCO C ANDRE R TAVARES C DIAS M GULYURTLU I CABRITA I | 2003 | Fuel2003，82，1517： | 1 |
| 7 | Automatic small bowel tumor diagnosis by u?sing multi-scale wavelet-based analysis in wireless cap?sule endoscopy images显示文摘 | Barbosa D C Roupar D B RamosJ C Tavares A C Li?rna C S | 2012 | Biomed Eng Online2012，11，： | 1 |
| 8 | Optimization of the extraction conditions of the volatile compounds from chili peppers by headspace solid phase micro- extraction显示文摘 | Bogusz Junior S de Marchi Tavares de Melo A Zini C A | 2011 | Journal of Chromatography A2011，1218，21： | 1 |
| 9 | The σ phase formation in annealed UNS S31803 duplex stainless steel: Texture aspects显示文摘 | Souza C M Abreu H F G Tavares S S M | 2008 | Materials Characterization2008，59，9： | 1 |
| 10 | Optimal generation scheduling of hydro-thermal power system显示文摘 | Lyra C Tavares H | 1980 | IEEE Trans on Power Apparatus and Systems1980，99，3： | 1 |
| 11 | Design and Implementation of a Biologically Realistic Olfactory Cortex in Analog VLSI显示文摘 | Principe Jose C Tavares Vitor G Harris John G Freeman Walter J | 2001 | Proceedings of the IEEE2001，89，7： | 1 |
| 12 | Oxidation of CO,ethanol and toluene over TiO2 supported noble metal catalysts显示文摘 | SANTOS V P CARABINEIRO S A C TAVARES P B PEREIRA M F R ORFAO J J M FIGUEIREDO J L | | 0，，： | 1 |
| 13 | The adhesion between fiber posts and root canal walls: comparison be-tween microtensile and push-out bond strength measure- ments显示文摘 | Goracci C Tavares AU Fabianelli A | 2004 | EurJOralSci2004，112，4： | 1 |
| 14 | Cardiovascular responses to L - glutamate microinjestion into the hupothalamie paraventricular nucleus are mediated by a local nitric oxide - guanylate cyelase mech- anism显示文摘 | Busnardo C Crestani CC Tavares RF | 2010 | Brain Res2010，1344，： | 1 |
| 15 | Antimicrobial photodynamic therapy: study of bacterialrecovery viability and potential development of resistanceafter treatment 显示文摘 | Tavares A Carvalho C M Faustino M A | 2010 | Mar Drugs2010，8，1： | 1 |
| 16 | Modeling on agriculture production greenhouse显示文摘 | O C Tavares A Goncalves P Catro | 2001 | Renewable energy2001，，22： | 1 |
| 17 | Femtosecond laser versus mechanical microkera- tomes for flap creation in laser in situ keratomileusis and effect of postoperative measurement interval on estimated femtosec- ond flap thickness 显示文摘 | Rosa AM Neto-Murta J Quadrado M J Tavares C Lobo C Van Velze R | 2009 | J Cataract Refract Surg2009，35，5： | 1 |
| 18 | Sulfate removal from waste chemicals by precipitation 显示文摘 | Benatti C T Tavares C R G Lenzi E | 2009 | Journal of Environmental Management2009，90，1： | 1 |
| 19 | Inflammation in chronic kidney disease: the role of cytokines 显示文摘 | Vianna H R Soares C M Tavares M S | 2011 | JBras Nefrol2011，33，3： | 1 |
| 20 | Generating and counting binary bent sequences显示文摘 | C M Adams S E Tavares | 1990 | IEEE Trans on Information Theory1990，36，5： | 1 |
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