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| 1 | Recent advances in chronic granulomatous disease显示文摘Chronic granulomatous disease(CGD)is an inherited defect of phagocyte function due to defective NADPH oxidase.Patients with CGD are not able to effectively clear the infections because of the defect in the phagocyte production of oxygen free radicals and are prone to recurrent bacterial and fungal infections.Inflammatory complications are also noted in CGD such as colitis,non-infective granulomas causing gastrointestinal or urinary tract obstruction,hemophagocytic lymphohistiocytosis,and arthritis.Studies on toll-like receptor pathways and neutrophil extracellular traps in CGD have shed light on the role of NADPH oxidase in the innate immunity and pathogenesis of infections in CGD.Some reports also indicate a reduction of memory B cells and defective production of functional antibodies in CGD.Though the exact mechanisms for non-infective inflammatory complications in CGD are not yet clear,studies on efferocytosis and defective autophagy with inflammasome activation have made a substantial contribution to our understanding of the pathogenesis of inflammation in CGD.We also discuss the clinical and molecular features of p40phox defects and a newer genetic defect,EROS.Clinical phenotypes of X-linked carriers of CYBB are also discussed. | Gummadi Anjani Pandiarajan Vignesh Vibhu Joshi Jitendra Kumar Shandilya Dharmagat Bhattarai Jyoti Sharma Amit Rawat | 2020 | Genes & Diseases2020,7,1: | 6 |
| 2 | Electrochemical ageing study of mixed lanthanum/praseodymium nickelates La2-xPrxNiO4+δ as oxygen electrodes for solid oxide fuel or electrolysis cells显示文摘The chemical and electrochemical stability of lanthanide nickelates La2 NiO4+δ(LNO),Pr2 NiO4+δ(PNO)and their mixed compounds La(2-x)PrxNiO4+δ(LPNOs)with x=0.5,1 or 1.5 is reported.The aim is to promote these materials as efficient electrodes for solid oxide fuel cell(SOFC)and/or solid oxide electrolysis cell(SOEC).La2 NiO4+δand La1.5Pr0.5NiO4+δcompounds are chemically very stable as powders over one month in the temperature range 600-800℃,while the other materials rich in praseodymium progressively decompose into various perovskite-deriving components with additional Pr6 O11.Despite their uneven properties,all these materials are quite efficient and sustainable as electrodes on top of gadolinium doped ceria(GDCBL)//yttrium doped zirconia(8 YSZ)electrolyte,for one month at 700℃without polarization.Under polarization(300 mA·cm-2),the electrochemical performances of LNO,PNO and La1.5Pr0.5NiO4+δ(LP5 NO)quickly degrade in SOFC mode,i.e.for the oxygen reduction reaction,while they show durability in SOEC mode,i.e.for the oxide oxidation reaction. | Vaibhav Vibhu Aurélien Flura Aline Rougier Clément Nicollet Sébastien Fourcade Teresa Hungria Jean-Claude Grenier Jean-Marc Bassat | 2020 | Journal of Energy Chemistry2020,29,7: | 6 |
| 3 | Management of neglected cervical spine dislocation: a study of six cases显示文摘没有神经病学的赤字的六忽视的颈的脊骨脱臼的一个案例系列,它是管理了 operatively.MethodsThe 学习的 ObjectiveTo 报告从 2010 年 8 月被进行到 2011 年 12 月,案例从医药教育和研究的研究生研究所的门诊部被选择,印度。病人在 30 ~ 50 年的年龄组。所有病人经由前面、以后的 approaches.ResultsDuring 被操作立即的手术后的时期,五(83.33%) 病人们有正常神经病学的地位。有 C 5-C6 subluxation 的(16.67%)病人在在更低的手足的 2/5 和在在 C 6 level.ConclusionThere 下面的上面的手足的 3/5 的水平和马达功率是的 C 6下面与感觉损失开发了神经病学的赤字在对颈的脊骨的忽视的分散注意力的屈曲损害的颅骨拖拉的角色都没为更多推迟比 3 个星期。以后由前面的途径列在后面节省许多时间。如果两条途径将在一样的坐被做,其次地对乐器学没有需要。但是如果上演过程是 planed,以后的稳定被推荐,,有在神经病学的地位的恶化的风险。 | Vijay Goni Nirmal Raj Gopinathan Vibhu Krishnan Rajesh Kumar Avinash Kumar | 2013 | Chinese Journal of Traumatology2013,16,4: | 6 |
| 4 | Ipsilateral fracture dislocations of the hip and knee joints with contralateral open fracture of the leg: a rare case and its management principles显示文摘这份报纸讨论了损害机制和有的伴随物 ipsilateral 臀部和膝脱臼和 contralateral 打开腿骨折的一个病人的管理。一个 32 岁的人与左臀部(小瓦锅的类型 IV ) 和关节和 contralateral 张开的膝(穆尔二世) 的 ipsilateral 破裂脱臼介绍了在一个汽车事故以后的腿骨头的骨折。在紧急情况以后使复生的措施,新潮的关节被减少,小瓦锅的破裂用 Ganz 途径被修理与落后螺丝钉;膝关节仔细被减少,胫骨的高原骨折与跨越 fixator 的侧面的撑墙板和 transarticular 被稳定。另外的腿上的开的破裂与外部 fixator 被清除并且修理。当他在麻醉下面被检查时,在在固定以后的两个关节没有不稳定性。破裂在 3 个月以后联合起来,病人没有臀部和膝的剩余不稳定性。没有在在 6 个月以后的新潮的关节的 osteonecrosis 的临床或放射学的证据。在一个年后续,他在两个关节与运动的几乎正常范围有令人满意的功能的结果。Ipsilateral 臀部和膝脱臼是稀罕损害,更多的小心为早诊断被需要。及时适当干预能处于这种状况提供好功能的结果给病人。 | Ramesh Kumar Sen Sujit Kumar Tripathy Vibhu Krishnan Tarun Goyal Vanyambadi Jagadeesh | 2011 | Chinese Journal of Traumatology2011,14,3: | 5 |
| 5 | An updated review on activated PI3 kinase delta syndrome(APDS)显示文摘Activated Phosphoinositide 3-kinase d syndrome(APDS)is a newly recognised primary immunodeficiency disease.It has currently been a hot topic of clinical research and new data are emerging regarding its pathogenesis,clinical manifestations and treatment.Patients with APDS syndrome have significant autoimmune manifestations and lymphoproliferation.It is important to differentiate APDS from the usual polygenic CVID in view of the availability of targeted therapy like mTOR inhibitors such as Rapamycin and selective PI3Kd inhibitors.We provide a comprehensive review on this interesting disorder focusing light on its etiology,genetic research and emerging therapy. | Ankita Singh Vibhu Joshi Ankur Kumar Jindal Babu Mathew Amit Rawat | 2020 | Genes & Diseases2020,7,1: | 4 |
| 6 | A rare case of bicondylar Hoffa fracture associated with ipsilateral tibial spine avulsion and extensor mechanism disruption显示文摘远侧的腿节的 Intra 关节的花冠破裂(Hoffas 破裂) 是稀罕的。尽管在这些破裂的 bicondylar 参与与高速度 traumata 联合在文学被报导了,这些的出现断裂包含伸肌机制破裂和 ipsilateral 的撕裂胫骨的脊骨极其稀罕。到我们的相识,如此的一个破裂模式到目前为止还没在文学被报导了。在这篇文章,我们报导一个如此的案例并且在如此的 cases.We 的管理讨论早诊断和迅速的内部固定的重要性相信损害的这些稀罕联合应该被早开的减小和解剖僵硬内部固定好攻击地对待以便完成好恢复工作。 | Kamal Bali Aditya Krishna Mootha Vibhu Krishnan Vishal Kumar Saurabh Rawall | 2011 | Chinese Journal of Traumatology2011,14,4: | 3 |
| 7 | An updated review on phenocopies of primary immunodeficiency diseases显示文摘Primary immunodeficiency diseases(PIDs)refer to a heterogenous group of disorders characterized clinically by increased susceptibility to infections,autoimmunity and increased risk of malignancies.These group of disorders present with clinical manifestations similar to PIDs with known genetic defects but have either no genetic defect or have a somatic mutation and thus have been labelled as“Phenocopies of PIDs”.These diseases have been further subdivided into those associated with somatic mutations and those associated with presence of auto-antibodies against various cytokines.In this review,we provide an update on clinical manifestations,diagnosis and management of these diseases. | Ankita Singh Ankur K.Jindal Vibhu Joshi Gummadi Anjani Amit Rawat | 2020 | Genes & Diseases2020,7,1: | 3 |
| 8 | Long term surgical treatment outcome of talar body fracture显示文摘lObjectiveTalar 身体破裂是稀罕的并且有差的处理结果。学习是报导关上的 talardome fractures.MethodsEight 的长期的外科的治疗结果的这的目的关上了 talar 身体破裂,在我们的水平与小碎片 cancellous 螺丝钉或 Herbert 螺丝钉由开的减小和内部固定对待我损伤中心回顾地被分析。脚(antero 以后、侧面、倾斜的看法) 和脚关节的外科手术前、手术后的拍(antero 以后,侧面并且榫眼看法) 被获得。病人被跟随在上面放射学地并且机能上地(脚功能索引, FFI ) 在 3 以后,星期, 6 个星期, 3 个月, 6 个月然后 annually.ResultsThere 是五压碎破裂并且三砍破裂(二 sagittal 砍并且一个花冠砍) ,与 5 年的平均后续。没有早复杂并发症在这些病人被注意。迟了的复杂并发症在四个病人在 talar 身体的六个病人和 osteonecrosis 包括了 subtalar/ankle 关节的 osteoarthrosis。在功能的评价以后,在 5 年以后的吝啬的 FFI 是 104.63 个点,更坏的结果在压碎损害和花冠被注意砍破裂。Sagittal 砍破裂有对通过手术对待的 talar 身体破裂随后的复杂并发症是的好功能、放射学的 outcome.ConclusionsLate 不可避免尽管准确减小和僵硬固定被完成,因此,病人们应当关于不利结果被建议。尽管压碎和花冠砍,破裂有差的结果, sagittal 损害在长期的评估上有好预后。 | Ramesh Kumar Sen Sujit Kumar Tripathy Shakthivel RR Manoharan Vibhu Krishnan Tajir Tamuk Vanyambadi Jagadeesh | 2011 | Chinese Journal of Traumatology2011,14,5: | 2 |
| 9 | A randomized controlled trial comparing lactulose, probiotics, and L-ornithine L-aspartate in treatment of minimal hepatic encephalopathy显示文摘 | Vibhu Vibhas Mittal Barjesh Chander Sharma Praveen Sharma Shiv Kumar Sarin | 2011 | European Journal of Gastroenterology & Hepatology2011,,8: | 2 |
| 10 | Neuroradiologic-patho- logic correlation in a neurenteric cyst of the clivus 显示文摘 | Vibhu KDR Douglas R J Melanie BF | 2002 | AJNR2002,23,: | 1 |
| 11 | A randomized controlled trial comparing lactulose, probiotics, and L-ornithine L-aspartate in treatment of minimal hepatic encephalopathy显示文摘 | Vibhu Vibhas Mittal Barjesh Chander Sharma Praveen Sharma Shiv Kumar Sarin | 2011 | European Journal of Gastroenterology & Hepatology2011,,8: | 1 |
| 12 | A randomized controlled trial comparing lactulose, probiotics, and L-ornithine L-aspartate in treatment of minimal hepatic encephalopathy显示文摘 | Vibhu Vibhas Mittal Barjesh Chander Sharma Praveen Sharma Shiv Kumar Sarin | 2011 | European Journal of Gastroenterology & Hepatology2011,,8: | 1 |
| 13 | Early, reliable, utilitarian predictive factors for fat embolism syndrome in polytrauma patients显示文摘 | Nirmal Raj Gopinathan Ramesh K Sen Vibhu K Viswanathan | 2013 | Indian journal of critical care medicine:peer-reviewed official publication of Indian Society of Critical Care Medicine2013,17,1: | 1 |
| 14 | Impulse response of Ge2Sb2Te5-based ultrafast photodetector integrated with SOI waveguide显示文摘The impulse response for a phase-change material Ge2Sb2Te5(GST)-based photodetector integrated with a silicon-on-insulator(SOI)waveguide is simulated using finite difference time domain method.The current is calculated by solving the drift-diffusion model for short pulse(?10 fs)excitation for both of the stable phases.Full width at half-maximum values of less than 1 ps are found in the investigation.The crystalline GST has higher 3 dB bandwidth than the amorphous GST at a 1550 nm wavelength with responsivities of 21 A/W and 18.5 A/W,respectively,for a 150 nm thick GST layer biased at 2 V.A broad spectrum can be utilized by tuning the device using the phase-change property of material in the near infrared region. | Vibhu Srivastava Prateek Mishra Sunny | 2019 | Chinese Optics Letters2019,17,10: | 1 |
| 15 | Evolving Market Design in Zero-Intelligence Trader Markets 显示文摘 | Vibhu Walia Andrew Byde Dave Cliff | 2003 | IEEE2003,,: | 1 |
| 16 | Intimomedial Rupture:A New CT Finding to Distinguish True from False Lumen in Aortic Dissection显示文摘 | Vibhu K James V Ferris | 2004 | AJR2004,,: | 1 |
| 17 | Ultrasonic ve- locity, viscosity and excess properties of binary mix- ture of tetrahydrofuran with 1-propanol and 2-propanol 显示文摘 | GUPTA M VIBHU I SHUKLA J P | 2006 | Fluid Phase Equilibria2006,244,1: | 1 |
| 18 | latrogenic aortic pseudoaneurysm following anterior tho- racic spine surgery masquerading as chronic infection显示文摘 | Vijay Goni A jay Bahl Nirmal Raj Gopinathan Vibhu Krishnan Rajesh Kumar | 2013 | Chinese Journal of Traumatology2013,16,6: | 1 |
| 19 | Identification of a constitutively active variant of LuxO that affects production of HA/protease and biofilm development in a non-O1,non-O139 Vibrio cholerae O110显示文摘 | Saumya Raychaudhuri Vibhu Jain Mitesh Dongre | 2006 | Gene2006,369,: | 1 |
| 20 | Refractive index, molar refraction deviation and excess molar volume of binary mixtures of 1,4-dioxane with carboxylic acids 显示文摘 | GUPTA M VIBHU I SHUKLA J P | 2010 | Phys Chem Liq2010,48,4: | 1 |